Nous rapportons le cas de Mr R. Langerhans cell histiocytosis is a rare disease of unknown etiology characterized by the infiltration of Langerhans cells in one or more organs. It has a polymorphic clinical presentation. We report the case of Mr R. Y, age 22, with 8 pack year history of smoking, admitted to hospital with complete spontaneous right-sided pneumothorax. Chest drainage was performed with good evolution.
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Blueberry Muffin Baby is a rare neonatal cutaneous syndrome for purpuric lesions reflective of extramedullary hematopoiesis. Many causes are known, examples are congenital infections, malignancy and hematologic disorders.
This has very rarely been associated with a Blueberry Muffin Baby presentation. At birth, he had multiple purpuric lesions on the trunk, limbs and face. Skin biopsy showed a dermal proliferation of histiocytes staining positive for S and CD1a. Chest and bone radiographs, and abdominal ultrasound were normal.
Skin lesions have resolved in 8 weeks, the patient is in complete remission at 18 months of follow-up. Journal page Archives Contents list. Schoeffler, E. Levy, M. Weinborn, J. Cuny, J.
Schmutz, A. Barbaud, B. Cribier, A. Article Article Outline. Access to the text HTML. Access to the PDF text. Recommend this article. Save as favorites. Access to the full text of this article requires a subscription. If you are a subscriber, please sign in 'My Account' at the top right of the screen. Charkaluk b , P. Gosset c , P. Outline Masquer le plan. Top of the page - Article Outline. Contact Help Who are we? As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that law , access art 34 of that law and rectify art 36 of that law your personal data.
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Histiocytose langerhansienne mandibulaire unifocale : a propos d’un cas
Langerhans cell histiocytosis ex histiocytosis X is usually present in children. Histological aspects are variable. The diagnosis is made in immunolabeling by anti-CD1a. Clinical presentations are variable, depending on their extension. Previous Article Kyste du canal nasopalatin L. Ben Slama, A.
We'd like to understand how you use our websites in order to improve them. Register your interest. Langerhans cell histiocytosis is easy to misdiagnose because of its various clinical aspects. It mainly affects children and young adults and can affect one or more organs bone, skin, lung, pituitary, lymphoid organs, central nervous system , its management is well codified in children; however, they are not consensual in adults. The aim of our work is to specify the clinical, histopathological, immunohistochemical, and evolutionary characteristics of Langerhans cell histiocytosis in order to improve diagnosis and decrease misdiagnosis rate. We report a case of cutaneous histiocytosis considered for 8 years as an extradigestive cutaneous manifestation of hemorrhagic colitis in a year-old man.